Anesthesia Management in Bart's syndrome: A Case Report
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Tarih
2022
Yazarlar
Dergi Başlığı
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Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Bart's syndrome is a genetic disorder that is also associated with epidermolysis bullosa (EB), which is characterized by congenital focal absence of the skin, mechanical bullous, and nail dystrophy. We present the anesthesia management of a male neonate with congenital localized skin absence, nail dystrophy, and ear atrophy who underwent surgery due to congenital pyloric atrophy. Palliative measures were perforemed paying attention to skin lesions in areas of rich-red peeling on the hands and feet of the patient, and standard general inhalation anesthesia was administered. As far as I could research in the English literature, this case report may be the first case report to present the management of anesthesia in a patient with Bart syndrome
Açıklama
Anahtar Kelimeler
Bart's syndrome, Case report, Congenital absence of the skin, Congenital pyloric atresia, Epidermolysis bullosa
Kaynak
Acta Medica Alanya
WoS Q Değeri
Scopus Q Değeri
Cilt
6
Sayı
1
