Anesthesia Management in Bart's syndrome: A Case Report
Özet
Bart's syndrome is a genetic disorder that is also associated with epidermolysis
bullosa (EB), which is characterized by congenital focal absence of the skin,
mechanical bullous, and nail dystrophy. We present the anesthesia management of a
male neonate with congenital localized skin absence, nail dystrophy, and ear atrophy
who underwent surgery due to congenital pyloric atrophy. Palliative measures were
perforemed paying attention to skin lesions in areas of rich-red peeling on the hands
and feet of the patient, and standard general inhalation anesthesia was administered.
As far as I could research in the English literature, this case report may be the first
case report to present the management of anesthesia in a patient with Bart syndrome
Kaynak
Acta Medica AlanyaCilt
6Sayı
1Bağlantı
https://dergipark.org.tr/tr/download/article-file/1894969https://hdl.handle.net/20.500.12868/1758